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corticobasal-degeneration, and late . [@teixeira2017] ## AGD Pathogenesis Pathway ### Key Pathogenic
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Corticobasal Degeneration (CBD) corticobasal-degeneration is a 4-repeat tauopathy
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Corticobasal Degeneration corticobasal-degeneration: - Asymmetric cortical atrophy, typically affecting posterior
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Corticobasal Degeneration corticobasal-degeneration (CBD) frequently involves asymmetric frontoparietal cortical
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Corticobasal Degeneration corticobasal-degeneration features asymmetric putaminal atrophy contralateral to the affected
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corticobasal-degeneration**: Asymmetric frontoparietal cortical atrophy contralateral to the clinically
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corticobasal-degeneration](/diseases/corticobasal-degeneration), FTLD-[tau](/proteins/tau) | | Anti-[alpha-synuclein](/proteins/alpha-synuclein
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Corticobasal Degeneration (CBD)corticobasal-degeneration) - [Microglia](/cell-types/microglia) - [Astrocytes](/cell-types/astrocytes) - [Neuroinflammation
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Corticobasal Degeneration (CBD)corticobasal-degeneration) - [Microglia](/cell-types/microglia) - [Astrocytes](/cell-types/astrocytes) - [Neuroinflammation
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Corticobasal Degeneration (CBD)corticobasal-degeneration) - [Microglia](/cell-types/microglia) - [Astrocytes](/cell-types/astrocytes) - [Neuroinflammation
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Corticobasal Degeneration In corticobasal-degeneration, the globus pallidus shows asymmetric
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Corticobasal Degeneration (CBD) corticobasal-degeneration involves asymmetric cortical and basal
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Corticobasal Degeneration (CBD)corticobasal-degeneration) - [Microglia](/cell-types/microglia) - [Astrocytes](/cell-types/astrocytes) - [Neuroinflammation
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Corticobasal Degeneration (CBD)corticobasal-degeneration) - [Tau Protein](/proteins/tau) - [MAPT Gene
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degeneration with glial cytoplasmic inclusions in oligodendrocytes - **Progressive Supranuclear Palsy**: Neuronal loss in the SNc with tau] pathology - **corticobasal
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corticobasal-degeneration-—-disease-association --ataxia-—-clinical-symptom --spinocerebellar-ataxia-—-related
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degeneration](/diseases/frontotemporal-lobar-degeneration) (FTLD)**: Most common cause - FTLD-tau]: Including Pick's disease [@irwin2016]- FTLD-TDP: TAR DNA-binding protein 43 inclusions [@neumann2006]- **[alzheimers](/diseases/alzheimers-disease)**: Particularly in logopenic variant [@gefen2018]- **[corticobasal
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corticobasal-degeneration]. ### Assessment Clinical assessment of simultanagnosia includes: | Test | Description
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corticobasal-degeneration](/diseases/corticobasal-degeneration), and [pick-disease](/diseases/pick-disease). - [c9orf72](/genes/c9orf72) repeat
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corticobasal-degeneration](/diseases/corticobasal-degeneration)**: Features astrocytic plaques, tau-positive threads, and ballooned
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corticobasal-degeneration](/diseases/corticobasal-degeneration). While [anti-amyloid-therapeutics](/mechanisms/anti-amyloid-therapeutics) such as [lecanemab
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corticobasal-degeneration](/diseases/corticobasal-degeneration) 2. **Autoimmune/inflammatory** — [autoimmune-encephalitis](/diseases/autoimmune-encephalitis), [neurosarcoidosis](/diseases/neurosarcoidosis
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